Truncus Arteriosus, Persistent

• Accounts for <1% of all CHD
• Both ventricles empty into a single vessel which supplies the systemic, pulmonary and coronary circulations
• RV and LV are always connected by a large VSD (therefore their pressures are equal)
• the VSD is barely audible
• pulmonary arteries branch off of the outflow tract
• SaO2 is proportional to pulmonary blood flow
• Right aortic archpresent in 30% of cases

Presentation: neonate with cyanosis and tachypnea

PE: systolic murmur (VSD), single S2

EKG: Biventricular hypertrophy

CXR: Right sided aortic arch, increased pulmonary vasculature,cardiomegaly

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TAPVR (5 letters) Total anomalous pulmonary venous return
Tetralogy of Fallot (tetra=4)
Transposition of the Great Arteries (2 arteries)
Tricuspid Atresia (tri=3)
Truncus Arteriosus (1 trunk)

CHLA Board Review 2005.
Park MK. Pediatric Cardiology for Practictioners, 3rded. St. Louis,
 Mosby, 1996.